The sixty two-year-old woman was admitted with facial diplegia and ataxic gait. Neurological examination revealedareflexia and sensory ataxia with decreased sensation of position and vibration in both lower extremities.Electrophysiologic study suggest motor dominant demyelinating polyneuropathy and bilateral facial neuropathy. CSFstudy revealed no cells and increased proteins. After intravenous immunoglobulin therapy, sensory ataxia and electrophysiologicalstudy had markedly improved for 3 months.