A 73-year-old man with progressive quadriparesis was diagnosed as Guillain-Barré syndrome. On the 6th hospital day, thepatient complained of sudden chest discomfort. The blood test and echocardiography suggested myocardial injury, and acutemyocardial infarction was considered. However, coronary angiography displayed no vascular lesion, and the electrocardiographyand echocardiogram showed marked improvement 14 days later. We concluded the patient had a reversible cardiomyopathywhich is a rare complication of Guillain-Barré syndrome.

Background
Although quantitative sensory test (QST) is being used with increasing frequency for measuring sensorythresholds in clinical practice and epidemiologic studies, there has been no age-matched normative data in Korean adults.The objective of this study is to evaluate the value of QST in diabetic polyneuropathy with normal range in Korean adults.Methods: The Computer Aided Sensory Examination IV 4,2 (WR Medical Electronics Co., Stillwater, Minnesota, U.S.A.),with 4,2,1 stepping algorithm was used to determine vibration and cold perception threshold in 70 normal controls and 19patients with diabetic polyneuropathy aged from 21 to 79 years. The data were used to define age-matched upper and lowernormal limits and normal range of side to side difference. We also evaluated the duration of diabetes, serum HbA1C level,and findings of nerve conduction study (NCS) and QST in patients with diabetic polyneuropathy. Results: In normal adults,sensory thresholds slightly increased with age, and a slight side-to-side difference was observed. The diagnostic sensitivityof QST was not higher than NCS in patients with diabetic polyneuropathy (36.8% vs. 42.1%, p=0.716), especially amongelderly patients. Conclusions: QST might be used as a complementary test for NCS in the diagnosis of diabeticpolyneuropathy. Although the QST is a simple method for the evaluation of peripheral nerve function, there are somelimitations. Most of all, because the QST measuring is dependent on the subjective response of patients, the degree of concentrationand cooperation of the patients can significantly affect the result. And thus, attention should be paid during theinterpretation of QST results in patients with peripheral neuropathy.

We report a 23-year-old woman with adult Sandhoff disease, who presented with motor neuron disease phenotype. The patient had experienced progressive motor weakness in four extremities since 1 year prior to admission. Electrophysiological study revealed wide-spread denervation potentials, and the assay of total hexosaminidase involving A and B activities showed decreased levels of these activities, which was consistent with Sandoff disease. This is the first Korean case of adult Sanhoff disease presented as a motor neuron disease phenotype.

Meralgia paresthetica (MP) is a benign entrapment neuropathy which is characterized by sensory impairment and paresthesia in the cutaneous distribution of the lateral femoral cutaneous nerve. A 79-year-old woman presented with intermittent right inguinal burning sensation. The sensory nerve conduction study (NCS) showed decreased right sidesensory nerve action potential (SNAP) on lateral femoral cutaneous nerve compared to the contralateral one. Abdomino-pelvic CT showed bilateral huge renal cysts (The size of largest one on right side: about 6.2